mrjСовременная ревматологияModern Rheumatology Journal1996-70122310-158XIMA-PRESS, LLC10.14412/1996-7012-2024-1-84-89mrj-1536Research ArticleКЛИНИЧЕСКИЕ НАБЛЮДЕНИЯCLINICAL OBSERVATIONSКлинический случай системной склеродермии у мужчины: гендерные различия и возможности капилляроскопииClinical case of systemic sclerosis in a male patient: gender differences and possibilities of capillaroscopyhttps://orcid.org/0000-0001-5926-7912ТрофимоваА. С.TrofimovaA. S.

195015, Санкт-Петербург, ул. Кирочная, 41

41, Kirochnaya Street, St. Petersburg 195015

anna.trofimova@szgmu.ruhttps://orcid.org/0009-0000-5440-237XШохинА. А.ShokhinA. A.

195015, Санкт-Петербург, ул. Кирочная, 41

41, Kirochnaya Street, St. Petersburg 195015

https://orcid.org/0000-0003-3236-4485ТрофимовЕ. А.TrofimovE. A.

195015, Санкт-Петербург, ул. Кирочная, 41

41, Kirochnaya Street, St. Petersburg 195015

https://orcid.org/0000-0001-5449-7372ШостакМ. С.ShostakM. S.

195015, Санкт-Петербург, ул. Кирочная, 41

41, Kirochnaya Street, St. Petersburg 195015

ФГБОУ ВО «Северо-Западный государственный медицинский университет им. И.И. Мечникова» Минздрава РоссииРоссияNorth-Western State Medical University named after I.I. Mechnikov, Ministry of Health of RussiaRussian Federation2024200220241818489Copyright © Трофимова А.С., Шохин А.А., Трофимов Е.А., Шостак М.С., 20242024Трофимова А.С., Шохин А.А., Трофимов Е.А., Шостак М.С.Trofimova A.S., Shokhin A.A., Trofimov E.A., Shostak M.S.Данная работа распространяется под лицензией Creative Commons Attribution 4.0.This work is licensed under a Creative Commons Attribution 4.0 License.https://mrj.ima-press.net/mrj/article/view/1536

Описан пациент с подострым течением системной склеродермии (ССД) и трехфазным синдромом Рейно в дебюте. Диагноз установлен в соответствии с критериями ACR/EULAR 2013 г. В течение 8 мес после начала заболевания у пациента развилась классическая картина ССД с полиорганным поражением, а при проведении капилляроскопии сосудов ногтевого ложа были выявлены признаки активной стадии склеродермической ангиопатии. Проанализированы факторы неблагоприятного течения ССД.

A patient with a subacute course of systemic sclerosis (SSc) and a three-phase Raynaud's phenomenon at the onset of the disease is described. The diagnosis was made in accordance with the ACR/EULAR 2013 criteria. Within 8 months of disease onset, the patient developed the classic picture of SSc with multiple organ involvement, and nailfold capillaroscopy showed signs of the active stage of scleroderma angiopathy. The factors for an unfavorable course of SSc were analyzed.

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The authors declare that there are no conflicts of interest present.