mrjСовременная ревматологияModern Rheumatology Journal1996-70122310-158XIMA-PRESS, LLC10.14412/1996-7012-2015-4-92-97mrj-659Research ArticleОБЗОРЫREVIEWSНеонатальная волчанкаNeonatal lupusКошелеваН. М.KoshelevaN. M.

115522, Москва, Каширское шоссе, 34А

34A, Kashirskoe Shosse, Moscow 115522

nadkosheleva@yandex.ruАлекбероваЗ. С.AlekberovaZ. S.

115522, Москва, Каширское шоссе, 34А

34A, Kashirskoe Shosse, Moscow 115522

ФГБНУ Научно-исследовательский институт ревматологии им. В.А. НасоновойРоссияV.A. Nasonova Research Institute of RheumatologyRussian Federation201514012016949297Copyright © Кошелева Н.М., Алекберова З.С., 20162016Кошелева Н.М., Алекберова З.С.Kosheleva N.M., Alekberova Z.S.Данная работа распространяется под лицензией Creative Commons Attribution 4.0.This work is licensed under a Creative Commons Attribution 4.0 License.https://mrj.ima-press.net/mrj/article/view/659

Неонатальная волчанка (НВ) – симтомокомплекс, диагностируемый у новорожденных, матери которых часто страдают аутоиммунными ревматическими заболеваниями, и проявляющийся двумя основными признаками: поражением кожи и сердца. В статье приводятся данные из истории описания синдрома, современные представления о его патогенезе, рассмотрены клинические проявления заболевания, как типичные, так и более редкие; представлены подходы к терапии и профилактике НВ.

Neonatal lupus (NL) is a syndrome diagnosed in neonatal infants, whose mothers frequently suffer from autoimmune rheumatic diseases, manifested by two major signs: skin lesion and cardiac lesion. The paper gives data from the history of a description of the syndrome, as well as current ideas on its pathogenesis, considers both typical and rarer clinical manifestations of the disease, and presents approaches to NL therapy and prevention.

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The authors declare that there are no conflicts of interest present.