mrjСовременная ревматологияModern Rheumatology Journal1996-70122310-158XIMA-PRESS, LLC10.14412/1996-7012-2019-2-119-123mrj-920Research ArticleКЛИНИЧЕСКОЕ НАБЛЮДЕНИЕCLINICAL OBSERVATIONSРазвитие лимфангиолейомиоматоза у пациентки с болезнью Шёгрена: обзор литературы и описание случаяDevelopment of lymphangioleiomyomatosis in a female patient with Sjö gren's disease: a review of literature and a case reportХванЮ. И.KhvanYu. I.

115522, Москва, Каширское шоссе, 34А

34A, Kashirskoe Shosse, Moscow 115522

julija.hwan@gmail.comПальшинаС. Г.PalshinaS. G.

115522, Москва, Каширское шоссе, 34А

34A, Kashirskoe Shosse, Moscow 115522

ВасильевВ. И.VasilievV. I.

123056, Москва, Грузинский переулок, 3А

3A, Gruzinskiy pereulok, Moscow 123056

ФГБНУ «Научно-исследовательский институт ревматологии им. В.А. Насоновой»РоссияV.A. Nasonova Research Institute of RheumatologyRussian FederationКлиника МЕДСИРоссияMEDSI ClinicRussian Federation201920052019132119123Copyright © Хван Ю.И., Пальшина С.Г., Васильев В.И., 20192019Хван Ю.И., Пальшина С.Г., Васильев В.И.Khvan Y.I., Palshina S.G., Vasiliev V.I.Данная работа распространяется под лицензией Creative Commons Attribution 4.0.This work is licensed under a Creative Commons Attribution 4.0 License.https://mrj.ima-press.net/mrj/article/view/920

Кистозно-буллезная трансформация легких встречается при заболеваниях различного генеза: опухолевых, генетически детерминированных, ревматических, лимфопролиферативных, инфекционных. В статье приводится обзор литературы и клиническое наблюдение молодой пациентки, длительно страдавшей болезнью Шёгрена. Через 15 лет после начала заболевания у пациентки возникла кистозно-буллезная трансформация легких и ангиомиолипома почки, расцененные как проявление вероятного лимфангиолейомиоматоза.

Cystic and bullous lung transformation occurs in diseases of various origins: neoplastic, genetically determined, rheumatic, lymphoproliferative, and infectious diseases. The paper presents a review of the literature and a clinical case of a young female patient with a long history of Sjögren's disease. Fifteen years after the onset of the disease, the patient developed cystic and bullous lung transformation and renal angiomyolipoma, which are regarded as a manifestation of probable lymphangioleiomyomatosis.

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The authors declare that there are no conflicts of interest present.