Fibrosing arthropathy in juvenile scleroderma
https://doi.org/10.14412/1996-7012-2021-2-64-68
Abstract
The group of scleroderma diseases includes a number of clinical entities, the main symptom of which is skin tightening. Scleroderma is a prominent example of these diseases, characterized by excessive synthesis and deposition of collagen in organs and tissues. A patient with juvenile systemic scleroderma with induration of the skin and underlying tissues, and persistent contractures of large joints since childhood, is described. This clinical example illustrates disease course peculiarities and differential diagnosis of systemic and limited (focal) scleroderma and scleroderma-like conditions in pediatric patients. The feasibility of pathogenetic therapy aimed at improving patient's the quality of life with formed disease phenotype is shown.
About the Authors
D. A. Dibrov
ФГБНУ «Научно-исследовательский институт ревматологии им. В.А. Насоновой»
Russian Federation
Russian Federation
Danil Alekseevich Dibrov
34A, Kashirskoe Shosse, Moscow 115522
M. N. Starovoitova
V.A. Nasonova Research Institute of Rheumatology
Russian Federation
Russian Federation
34A, Kashirskoe Shosse, Moscow 115522
O. V. Desinova
V.A. Nasonova Research Institute of Rheumatology
Russian Federation
Russian Federation
34A, Kashirskoe Shosse, Moscow 115522
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Review
For citations:
Dibrov DA, Starovoitova MN, Desinova OV. Fibrosing arthropathy in juvenile scleroderma. Sovremennaya Revmatologiya=Modern Rheumatology Journal. 2021;15(2):64-68. (In Russ.) https://doi.org/10.14412/1996-7012-2021-2-64-68
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